Grant Recipients

2019 - 2020

STUART TANGYE, PhD
Garvan Institute of Medical Research, AUSTRALIA
STAT3-mediated regulation of the human immune response - unraveling the complexities of disease pathogenesis of Job's syndrome

ELLEN RENNER, MD
Helmholtz Zentrum München, GERMANY
Fighting Staphylococcus aureus infections at the mucosal surface in Job Syndrome

PETER OLBRICH, MD, PhD
OLAF NETH, MD, PhD

Hospital Infantil Universitario Virgen del Rocio, SPAIN
JAK-inhibition to prevent the development of pulmonary complications in autosomal dominant Hyper IgE Syndrome

BERTRAND BOISSON, PhD
The Rockefeller University, USA
Dissecting the mechanism of STAT3 dominance underlying Job's Syndrome


2020 - 2021

HONGMEI MOU, PhD
Massachusetts General Hospital / Harvard Medical School, USA
Impaired Epithelial Differentiation and Host Defense as a Mechanism for Pulmonary Complications in Job Syndrome Patients

ANDREW GENNERY, MD
ALEXANDRA FREEMAN, AUSTEN WORTH, RAFFAELE BADOLATO

University of Newcastle Upon Tyne, UK
Investigating Health Status and Quality of Life in Patients with Autosomal Dominant Hyper IgE Syndrome

VERA P. KRYMSKAYA, PhD, MBA, FCPP
ANDREW PARIS, MD

University of Pennsylvania, USA
Nanotechnology as a novel cellular therapy for patients with Job Syndrome

SCOTT SNAPPER, MD, PhD
Boston Children's Hospital, USA
Investigating a Non-Transcriptional Role for IL-10-STAT3 in Mitochondrial Metabolism and AD-HIES


2021 - 2022

TONI CATHOMEN, PhD
BODO GRIMBACHER, MD

University of Freiburg, GERMANY
Treating Hyper-IgE-Syndrome by genome editing in CD34+ hematopoietic stem and progenitor cells

MARK GORELIK, MD
Columbia University Vagelos School of Medicine, USA
The role of fibroblast specific STAT3 expression in pneumatocele development and gastrointestinal perforation in AD-HIES


2022 - 2023

BEATE HAGLE 
CAROLA VOSS (co-principal) 
Helmholtz Zentrum Munchen, GERMANY
Evaluation of alveolar function, regeneration and gene repair in Job Syndrome

SUK SEE DE RAVIN, MD, PhD 
Laboratory of Clinical Immunology and Microbiology, NIAID, USA
Next-generation CRISPR Base Editing Approaches to Treat Job Syndrome


2023 - 2024

MARIA A. CUROTTO DE LAFAILLE, PhD
Associate Professor, Icahn School of Medicine at Mount Sinai, USA
Cross-regulation of STAT signaling pathways in lung pathology of experimental HIES

STUART TANGYE, PhD
Senior Principal Research Fellow, Lab Head, Garvan Institute of Medical Research, AUSTRALIA
Immune dysregulation in Job Syndrome - elucidating mechanisms of STAT3-mediated host defense, humoral immunity and immune-mediated lung pathology


2024

DR. RASMUS O. BAK
Aarhus University, Denmark
Next generation CRISPR/Cas-based ex vivo Gene Editing of Autologous Hematopoietic Stem Cells as a Curative Treatment of Job Syndrome